Sclerema neonatorum: recovery with cortisone.
نویسنده
چکیده
practice. Occasionally intermediate cases have presented difficulty and some atypical examples, such as the case described by Nicholson and Claireaux (1948) which appeared to be a form of generalized infective cellulitis in an older baby, defy classification. A third condition, characterized by localized pitting oedema in cold premature babies, is sometimes called scleroedema but this is not always easy to differentiate from fat necrosis. Scleroderma with sclerodactyly is a disease of the skin which probably does not occur in infancy. The generalized disorder in young babies (to which the term scierema neonatorum will be confined here) was first recorded by Usenbenzius (1722) who described a newborn baby that was intensely cold and rigid. Underwood mentioned the condition in his book in 1784, but described it in full in a later edition (1819) under the heading 'skin bound'. He acknowledged assistance from Dr. Denman in making the following list of pathognomonic symptoms:
منابع مشابه
Fatty crystals in sclerema neonatorum.
The fatty crystals in three previously published cases of sclerema neonatorum were identified by means of x-ray diffraction as sodium stearate and palmitic acid. A composite view of the pathogenesis of both sclerema neonatorum and adiponecrosis cutis neonatorum is discussed.
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ورودعنوان ژورنال:
- Archives of disease in childhood
دوره 31 159 شماره
صفحات -
تاریخ انتشار 1956